APPENDIX 1

Diagnoses, Procedures, Tests, and Medications Relevant to Communication Impairment

ConditionsICD-9-CM Diagnostic, Health Factor, and Procedure CodesHigh ProbabilityModerate Probability
Creutzfeldt–Jakob disease046.1X
 Variant Creutzfeldt–Jakob disease046.11X
 Other and unspecified Creutzfeldt–Jakob disease046.19X
Progressive multifocal046.3X
Lipidoses272.7X
Mucopolysaccharidosis277.5X
Dementias290X
 Senile dementia, uncomplicated (senile dementia NOSa, simple type)290.0X
 Presenile dementia (brain syndrome with presenile brain disease)290.1X
  Presenile dementia, uncomplicated (presenile dementia, NOSa; simple type)290.10X
  Presenile dementia with delirium (presenile dementia with acute confusional state)290.11X
  Presenile dementia with delusional features (presenile dementia, paranoid type)290.12X
  Presenile dementia with depressive features290.13X
 Senile dementia with delusional or depressive features290.2X
  Senile dementia with delusional features290.20X
  Senile dementia with depressive features290.21X
  Senile dementia with delirium290.3X
 Vascular dementia290.4X
  Vascular dementia, uncomplicated290.40X
  Vascular dementia with delirium290.41X
  Vascular dementia with delusions290.42X
  Vascular dementia with depressed mood290.43X
 Dementia in conditions classified elsewhere294.1X
  Dementia in conditions classified elsewhere without behavioral disturbance294.10X
  Dementia in conditions classified elsewhere with behavioral disturbance294.11X
 Dementia unspecified294.2X
  Dementia, unspecified, without behavioral disturbance; dementia NOSa294.20X
 Dementia, unspecified, with behavioral disturbance294.21X
Pervasive developmental disorders299X
 Autistic disorder299.0X
 Childhood disintegrative disorder299.1X
 Other specified pervasive developmental disorders299.8X
 Unspecified pervasive developmental disorder299.9X
Intellectual disabilities
Mild intellectual disabilities317X
Other specified intellectual disabilities318X
 Moderate intellectual disabilities318.0X
 Severe intellectual disabilities318.1X
 Profound intellectual disabilities318.2X
Unspecified intellectual disabilities319X
Cerebral degenerations usually manifest in childhood330X
 Leukodystrophy330.0X
 Cerebral lipidoses330.1X
 Cerebral degeneration in generalized lipidoses330.2X
 Cerebral degeneration of childhood in other diseases classified elsewhere330.3X
 Other specified cerebral degenerations in childhood330.8X
 Unspecified cerebral degeneration in childhood330.9X
Other cerebral degenerations331X
 Alzheimer’s disease331.0X
 Frontotemporal dementia331.1X
  Pick disease331.11X
  Other frontotemporal dementia331.19X
 Senile degeneration of brain331.2X
 Corticobasal degeneration331.6X
 Cerebral degeneration in disease classified elsewhere331.7X
 Other cerebral degeneration331.8X
  Reye syndrome331.81X
  Dementia with Lewy bodies331.82X
  Mild cognitive impairment, so stated331.83X
  Other, cerebral ataxia331.89X
 Other cerebral degeneration, unspecified331.9X
 Other degenerative diseases of the basal ganglia333.0X
 Huntington chorea333.4X
 Other choreas333.5X
 Genetic torsion dystonia333.6X
  Athetoid cerebral palsy333.71X
  Stiff-man syndrome333.91X
Spinocerebellar disease334X
 Friedreich ataxia334.0X
 Hereditary spastic paraplegia334.1X
 Primary cerebellar degeneration334.2X
 Other cerebellar ataxia (NOSa)334.3X
 Cerebellar ataxia in diseases classified elsewhere334.4X
 Other spinocerebellar diseases334.8X
 Spinocerebellar disease, unspecified334.9X
Anterior horn disease335
 Werdnig–Hoffmann disease335.0X
 Motor neuron disease335.2X
  Amyotrophic lateral sclerosis335.20X
  Progressive muscular atrophy335.21X
  Progressive bulbar palsy335.22X
  Pseudobulbar palsy335.23X
  Primary lateral sclerosis335.24X
  Other335.29X
 Other anterior horn cell disease335.8X
 Anterior horn cell disease, unspecified335.9X
Infantile cerebral palsy343X
 Diplegic343.0X
 Hemiplegic343.1X
 Quadriplegic343.2X
 Monoplegic343.3X
 Other specified infantile cerebral palsy343.8X
 Infantile cerebral palsy, unspecified, NOSa343.9X
 Generalized convulsive epilepsy345.1X
Rheumatic chorea392X
 With heart involvement392.1X
 Without heart involvement392.9X
Late effects of cerebrovascular disease438
 Cognitive deficits438.0X
 Speech and language deficits438.1X
  Speech and language deficit, unspecified438.10X
  Aphasia438.11X
  Dysphasia438.12X
  Dysarthria438.13X
  Fluency disorder438.14X
  Other speech and language deficits438.19X
Anencephalus740X
 Other specified anomalies of nervous system742.8X
Chromosomal anomalies758X
 Down syndrome758.0X
 Patau syndrome758.1X
 Trisomy 18758.2X
 Autosomal deletion syndromes758.3X
  Cri-du-chat syndrome758.31X
  Velocardiofacial syndrome758.32X
  Other microdeletions758.33X
  Other autosomal deletions758.39X
 Other conditions due to autosomal anomalies758.5X
 Klinefelter syndrome758.7X
 Other conditions due to chromosome anomalies758.8X
  Other conditions due to sex chromosome anomalies758.81X
  Other758.89X
 Conditions due to anomaly of unspecified chromosome758.9X
 Multiple congenital anomalies759.7X
 Other specified anomalies759.8X
  Prader–Willi syndrome759.81X
  Marfan syndrome759.82X
  Fragile X syndrome759.83X
  Other759.89X
  Congenital anomaly, unspecified759.9X
aNOS, not otherwise specified.
Technology DependenciesICD-9-CM Diagnostic Codes (Treatment Codes)High ProbabilityModerate Probability
Tracheostomy
 Complete laryngectomy with tracheostomy30.3X
 Radical laryngectomy with tracheostomy30.4X
 Temporary tracheostomy operation31.1X
 Permanent tracheostomy31.2X
  Mediastinal tracheostomy31.21X
  Other permanent tracheostomy31.29X
TracheostomyV44.0X
Attention to tracheostomyV55.0X
Conditions associated with tracheostomy
 Tracheostomy complication, unspecified519.00X
 Infection of tracheostomy519.01X
 Mechanical complication of tracheostomy519.02X
 Other tracheostomy complications519.09X
Gastrotomy43.0X
 Gastrostomy43.1X
  Percutaneous endoscopic gastrostomy (percutaneous transabdominal gastrostomy)43.11X
  Other gastrostomy43.19X
  Replacement of gastrostomy tube97.02X
Gastrostomy (artificial opening status)V44.1X
Gastrostomy (attention to artificial openings)V55.1X
Gastrostomy complications536.4X
 Gastrostomy complication, unspecified536.40X
 Infection of gastrostomy536.41X
 Mechanical complication of gastrostomy536.42X
 Other gastrostomy complications536.49X
ProceduresICD-9-CM Diagnostic Codes (Treatment Codes)High ProbabilityModerate Probability
Intracranial ventricular shunt or anastomosis02.22X
Extracranial ventricular shunt02.3, 02.31–02.39X
Revision, removal, and irrigation of ventricular shunt02.4, 02.41–02.43X
Shunt, ventriculoperitoneal, ventricular site02.41, 02.42X
Irrigation and exploration of ventricular shunt, exploration of ventriculoperitoneal shunt at ventricular site, reprogramming of ventriculoperitoneal shunt02.41X
Replacement of ventricular shunt, reinsertion of Holter valve, replacement of ventricular catheter, revision of ventriculoperitoneal shunt at ventricular site02.42X
Other procedures for creation of esophagogastric sphincteric competence44.66X
Laparoscopic procedures for creation of esophagogastric sphincteric competence44.67X
Spinal fusion (spinal rod placement)81.0X
 Spinal fusion, not otherwise specified81.00X
 Refusion of spine81.3X
TestsICD-9-CM Diagnostic Codes (Treatment Codes)High ProbabilityModerate Probability
MRI of brain and brain stem88.91X
MRI head without contrast70551X
MRI head with contrast70551X
MRI head with and without contrast70553X
Barium swallow87.61X
Salivagram (CPTb codes)
 Salivary gland imaging78230X
 Serial salivary gland78231X
 Salivary gland function examination78232X
Gastroesophageal reflux examination78262X
Gastric emptying study78264X
Cerebrospinal fluid shunt evaluation (CPTb code)78645X
bCPT, Current Procedural Terminology.
MedicationsHigh ProbabilityModerate Probability
BethanecholX
ClonazepamX
ClonidineX
ClorazepateX
DiazepamX
DocusateX
GabapentinX
GlycopyrrolateX
Lactulose solutionX
LamotrigineX
LansoprazoleX
LevetiracetamX
LevocarnitineX
LorazepamX
MelatoninX
OmeprazoleX
PantoprazoleX
PentobarbitalX
PhenobarbitalX
Polyethylene glycolX
RanitidineX
RufinamideX
Scopolamine patchX
Sennosides syrupX
TopiramateX
Valproic acidX
VigabatrinX
ZonisamideX