Primary Condition and Medical Device Dependence in Patients With a PDN Care Plan Admitted to a Quaternary Freestanding Children’s Hospital (June 1, 2014 to May 31, 2015)
| Characteristic | Patients With PDN (n = 188) |
|---|---|
| n (%) | |
| Primary condition | |
| Genetic | 75 (40) |
| Genetic syndrome (eg, CHARGE syndrome, trisomy 21, etc) or genetic mutation not otherwise specified | 40 (21) |
| Muscular dystrophy, spinal muscular atrophy, or other neurodegenerative condition | 13 (7) |
| Metabolic or mitochondrial condition | 7 (4) |
| Congenital central hypoventilation | 6 (3) |
| Craniofacial syndrome | 5 (3) |
| Skeletal dysplasia | 4 (2) |
| Brain injury | 40 (21) |
| Cerebral palsy | 30 (16) |
| Other injury (eg, traumatic, infectious, autoimmune, etc) | 7 (4) |
| Intractable epilepsy or seizure disorder (NOS) | 3 (27) |
| Prematurity complications or sequelae (NOS) | 25 (13) |
| Multiple congenital anomalies (NOS) | 17 (9) |
| Intestinal failure (“short-gut syndrome”) | 16 (9) |
| Spinal cord | 10 (5) |
| Congenital (ie, spina bifida) | 6 (3) |
| Spinal cord injury (eg, infection, traumatic) | 4 (2) |
| Other (eg, renal dysplasia, airway anomaly, etc) | 5 (3) |
| Medical device used, by system | |
| Gastrointestinal | 176 (94) |
| Gastrostomy tube | 140 (74) |
| Gastrostomy-jejunostomy tube | 27 (14) |
| Nasogastric tube | 7 (4) |
| Ostomy | 2 (1) |
| Respiratory | 134 (71) |
| Invasive | 118 (63) |
| Tracheostomy and ventilator | 72 (38) |
| Tracheostomy (only) | 46 (25) |
| Noninvasive (eg, BiPAP, CPAP, nasal cannula) | 16 (9) |
| Neurology | 29 (15) |
| Shunt (eg, ventriculoperitoneal shunt) | 21 (11) |
| Baclofen pump | 4 (2) |
| Vagal nerve stimulator | 4 (2) |
| Vascular (ie, central line or port) | 18 (10) |
| Other (cardiac pacemaker, diaphragm pacer, cochlear implant, dialysis) | 10 (5) |
| None | 2 (1) |
Patients may have >1 medical device. BiPAP, bilevel positive airway pressure; CHARGE syndrome, coloboma, congenital heart disease, choanal atresia, mental and growth retardation, genital anomalies, and ear malformations and hearing loss; CPAP, continuous positive airway pressure; NOS, not otherwise specified.