Primary Condition and Medical Device Dependence in Patients With a PDN Care Plan Admitted to a Quaternary Freestanding Children’s Hospital (June 1, 2014 to May 31, 2015)

CharacteristicPatients With PDN (n = 188)
n (%)
Primary condition
 Genetic75 (40)
  Genetic syndrome (eg, CHARGE syndrome, trisomy 21, etc) or genetic mutation not otherwise specified40 (21)
  Muscular dystrophy, spinal muscular atrophy, or other neurodegenerative condition13 (7)
  Metabolic or mitochondrial condition7 (4)
  Congenital central hypoventilation6 (3)
  Craniofacial syndrome5 (3)
  Skeletal dysplasia4 (2)
 Brain injury40 (21)
  Cerebral palsy30 (16)
  Other injury (eg, traumatic, infectious, autoimmune, etc)7 (4)
  Intractable epilepsy or seizure disorder (NOS)3 (27)
 Prematurity complications or sequelae (NOS)25 (13)
 Multiple congenital anomalies (NOS)17 (9)
 Intestinal failure (“short-gut syndrome”)16 (9)
 Spinal cord10 (5)
  Congenital (ie, spina bifida)6 (3)
  Spinal cord injury (eg, infection, traumatic)4 (2)
 Other (eg, renal dysplasia, airway anomaly, etc)5 (3)
Medical device used, by system
 Gastrointestinal176 (94)
  Gastrostomy tube140 (74)
  Gastrostomy-jejunostomy tube27 (14)
  Nasogastric tube7 (4)
  Ostomy2 (1)
 Respiratory134 (71)
  Invasive118 (63)
   Tracheostomy and ventilator72 (38)
   Tracheostomy (only)46 (25)
  Noninvasive (eg, BiPAP, CPAP, nasal cannula)16 (9)
 Neurology29 (15)
  Shunt (eg, ventriculoperitoneal shunt)21 (11)
  Baclofen pump4 (2)
  Vagal nerve stimulator4 (2)
 Vascular (ie, central line or port)18 (10)
 Other (cardiac pacemaker, diaphragm pacer, cochlear implant, dialysis)10 (5)
 None2 (1)
  • Patients may have >1 medical device. BiPAP, bilevel positive airway pressure; CHARGE syndrome, coloboma, congenital heart disease, choanal atresia, mental and growth retardation, genital anomalies, and ear malformations and hearing loss; CPAP, continuous positive airway pressure; NOS, not otherwise specified.